Advanced PEX-syndrome with iridopathy (reduced mydriasis, atrophy of the stroma with superficial defects, atrophy of the pigment layer at pupillary margin, occasionally hemorrhages: all iris tissues are participants in the disease process. A PEX membrane is on the lens. The cornea is slightly hazy due to involvement of the endothelium.
Naumann, G.O.H., Prof. Dr. med., Univ.-Augenklinik, Erlangen, Germany