Atlas of Ophthalmology

先天性内皮ジストロフィー

先天性内皮ジストロフィー
8歳女児、広範な角膜の濁り、細隙灯検査では全層の濁りが観察される
Naumann, G.O.H., Prof. Dr. med., Univ.-Augenklinik, Erlangen, Germany
H18.53
Cornea -> Dystrophies, Genetic Keratopathies -> Endothelial Dystrophies -> Congenital Hereditary Endothelial Dystrophy (CHED)
6366
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